[01] Kianoush Saberi, Imam Khomeini Hospital, Tehran University of Medical Sciences, Tehran, Iran. [02] Mehrdad Salehi, Imam Khomeini Hospital, Tehran University of Medical Sciences, Tehran, Iran. [03] Mehrzad Rahmanian, Imam Khomeini Hospital, Tehran University of Medical Sciences, Tehran, Iran.

According to literature reviews, the paucity of infants with propionic academia was manifested. There are a variety of important medical issues associated with this genetic abnormality. Although there are an enormous range of methods and techniques to identify and treat metabolic defects, the requisite of an anesthesiologist for a specific plan, yet is not comprehensively answered. In this case, we have presented a 17-month old boy with propionic academia who was also suffered from frequent respiratory infection, tachypnea and failure to thrive; our echocardiography demonstrated both atrial septal defect (ASD) and patent ductus arteriosus (PDA). He was candidated for required closure surgery. In this article we provided information regarding propionic acidemia and its perioperative anesthetic implication especially in a cardiac surgery

Anaesthetic Techniques, Propionic Academia, ASD, Cardiac Surgery

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